P-ISSN 2587-2400 | E-ISSN 2587-196X
Ahead of Print | DOI: 10.14744/ejmo.2019.40823

Deep Sedation In Difficult Airway Patient: Case Report About Dental Treatment of Hurler Scheie Syndrome(MPS IH/IS) Patient

Seher Orbay Yasli1, Dilek Gunay Canpolat2
1Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Erciyes University, Kayseri, Turkey, 2DDepartment of Oral and Maxillofacial Surgery, Faculty of Dentistry, Erciyes University, Kayseri, Turkey

There are a wide range of special care patients in dentistry anesthesia. As a consequence of this condition, rare syndroms are encountered. Hurler-Scheie syndrome is an inherited disorder of mucopolysaceharide metabolism, which is caused by a defect in genetically controlled pathways of lysosomal degradation. As a result, mucopolysaccharide accumulation occurs in various tissues and organs. Structural and functional deficits resulting from Hurler-Scheie Syndrome can lead to difficulties in providing safe airway, especially during anesthetic applications. There is limited data on the literature about the deep sedation practice in patients with Hurler-Scheie syndrome. We aimed to describe our experience of deep sedation for dental treatment in a child with Hurler-Scheie syndrome.


Cite This Article

Orbay Yasli S, Gunay Canpolat D. Deep Sedation In Difficult Airway Patient: Case Report About Dental Treatment of Hurler Scheie Syndrome(MPS IH/IS) Patient. EJMO. ; (): -

Corresponding Author: Orbay Yasli S.

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